Successful Perioperative Hemostatic Management in Type 3 von Willebrand Disease During Laparoscopic Repair of Giant Hiatus Hernia Complicated by Pneumothorax

Jamal A. Abu Dina

المؤلفون

Jamal A. Abu Dina Department of Anesthesia and Intensive Care Care Unit Misurata Medical Center Misurata Libya

الكلمات المفتاحية:

von Willebrand disease، type 3، laparoscopic surgery، perioperative management، pneumothorax

الملخص

Background: Type 3 von Willebrand disease (vWD) is the most severe form of inherited bleeding disorders and carries a high perioperative hemorrhagic risk.

Case Presentation: A 33-year-old male with known type 3 vWD underwent elective laparoscopic repair of a grade IV hiatus hernia. Perioperative management included administration of von Willebrand factor/factor VIII (VWF/FVIII) concentrate. The postoperative course was complicated by left-sided pneumothorax requiring chest tube insertion. Replacement therapy continued for six days; no bleeding complications or transfusion were required.

Conclusion: Major laparoscopic surgery can be safely performed in patients with severe vWD when managed with appropriate replacement therapy and multidisciplinary coordination.

Keywords: von Willebrand disease; type 3; laparoscopic surgery; perioperative management; pneumothorax; hemostasis

المراجع

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